Pigmented paravenous retinochoroidal atrophy (PPRCA): a systematic review - International Ophthalmology Purpose Pigmented paravenous retinochoroidal atrophy (PPRCA) is a rare, poorly understood chorioretinal disorder characterised by perivenous atrophy and pigment clumping. This systematic review aimed ...

Our systematic review of 72 studies & 162 patients suggests PPRCA may be a phenotypic label, not one uniform disease. No standard diagnostic criteria yet, limited treatment pathways, a clear need for registries and collaborative research #PPRCA #SystematicReview

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